安塞| 大厂| 潞西| 阿拉善左旗| 于田| 云县| 罗田| 九寨沟| 和布克塞尔| 精河| 林芝县| 涪陵| 荥经| 浦口| 克拉玛依| 六安| 博野| 潼关| 亚东| 镇康| 富拉尔基| 垣曲| 石河子| 君山| 米脂| 古田| 海兴| 商水| 于都| 铜鼓| 灵台| 丹东| 蠡县| 德昌| 紫云| 泗洪| 集贤| 清水河| 广水| 兴县| 都兰| 祁阳| 通山| 新田| 太康| 通化县| 井研| 嵊州| 科尔沁左翼后旗| 舒城| 日土| 威海| 互助| 天安门| 紫云| 宁阳| 墨脱| 长泰| 宜宾市| 凤城| 德庆| 海原| 山阳| 茶陵| 灵璧| 正蓝旗| 恩平| 杭锦后旗| 沙圪堵| 环县| 巴青| 谷城| 贞丰| 西吉| 浦东新区| 新郑| 崂山| 新荣| 沁源| 石棉| 海南| 安泽| 连州| 鄯善| 泰宁| 清河| 密云| 都江堰| 枣庄| 雷州| 犍为| 武汉| 陇西| 延庆| 丘北| 盐亭| 昭觉| 丹东| 宁津| 磁县| 四方台| 鲅鱼圈| 白玉| 思茅| 双江| 皋兰| 陕西| 朗县| 宜宾县| 安达| 五原| 柏乡| 凤冈| 甘德| 山阴| 阿荣旗| 垦利| 泗洪| 磁县| 甘棠镇| 固镇| 鹤峰| 兴安| 昭苏| 聂荣| 康保| 晋城| 运城| 禄劝| 呼伦贝尔| 盱眙| 海淀| 西山| 民和| 昭苏| 金秀| 襄汾| 鄂州| 宿松| 会同| 平坝| 炎陵| 柘荣| 远安| 八一镇| 丰都| 聊城| 青冈| 玉树| 潘集| 湖州| 福贡| 佛山| 炉霍| 武平| 惠来| 贵定| 阿克塞| 精河| 崇明| 抚远| 潼南| 通江| 方城| 平江| 平度| 阳江| 桐梓| 拉萨| 高要| 临颍| 班玛| 西沙岛| 岳西| 塔城| 麻栗坡| 巴南| 泗洪| 府谷| 五营| 杜集| 黄梅| 永城| 宽城| 塔城| 西畴| 宝鸡| 淮滨| 睢宁| 应城| 于都| 淅川| 政和| 沭阳| 山海关| 永顺| 新津| 蒲县| 科尔沁左翼中旗| 新邱| 康平| 花都| 瓮安| 扶沟| 麦积| 尼勒克| 宜丰| 新泰| 巴林左旗| 定南| 和布克塞尔| 香河| 永昌| 安仁| 莘县| 大足| 拜城| 霍州| 下花园| 裕民| 苏尼特右旗| 大冶| 老河口| 连城| 长清| 稷山| 武隆| 静乐| 长垣| 阜新市| 永川| 东光| 上林| 珠海| 松江| 定远| 蓝山| 句容| 平房| 杨凌| 万山| 山海关| 威县| 郫县| 莒县| 凤县| 巴东| 孙吴| 衡山| 大同区| 郧西| 乐山| 遵义县| 芦山| 宁陕| 六合| 乌兰察布| 临淄| 古冶| 土默特左旗| 六合| 峡江| 饶平|

金曼:歌剧是一种共情 当下作品应是未来传统

2019-09-22 07:34 来源:有问必答

  金曼:歌剧是一种共情 当下作品应是未来传统

  活动结束后,所有成员一起上台,张朝阳为大家颁发了澳门站的奖牌。Suspectaccusedofcontractfraud;globalcampaignreachesmidpointAglobalcampaigntocatchChinasmost-wantedfugitivessawthereturnofits50thcorruptionsuspect,,47,whohasbeenontheruninHongKongfornineyears,-internationalarrestwarrants-storyresearchdepar,,halfofthe100corruptfugitiveshavebeenbroughtbackfrommorethan16countriesandregionstostandtrial,whichfullyreflects"Chinasfirmdeterminationandresoluteconfidencetopursuethefugitivestotheend",,anumberofChinesecorruptofficialsanddirectorsfromState-ownedcompanieshavefledtotheHongKongorMacaospecialadministrativeregionsoroverseasdestinationstotakead,theyhavesentmillionsofyuaninillegal,in2014,theCentralAnti-corruptionCoordinationGroup,ledbytheCCDI,launchedtheSkynetprogram,morethan2,600fugitivessuspectedofeconomiccrimeshadreturnedtoChinafromover90countriesandregionstofacecharges,includingtheUnitedStates,($)hadbeenrecovered."Wewillcontinueouractionsandleavenosafeheavenforthefugitives,"theCCDIsaidinastatement."Nomatterwheretheyarehiding,wewillmakeeveryefforttobringthembacktofacejustice."

,inthefirsthalfoftheyearChinasmaternitymortalityratereached183per1millionpeople,hinauntiltheendoflastyear,whenthetopleadershipapprovedtheadoptionoftheuniversaltwo-childpolicytotackletheproblemsposedbythenation,thedecades-longfamilyplanningpolicy,whichlimitedmostcouplestoonechild,,themortalityrateduringpregnancyfellto201per1millionpeoplefrom300per1millionin2010,accordingtothecommission,butthefigureisnowrising."Theriseinthenumberofpregnantwomen,particularlythoseathigherrisksuchasolderwomen,resultedinariseinmaternitydeathsinsomepartsofthecountryinthefirsthalfoftheyear,"regnantinChinaeveryyearbetweenthestartofnextyearand2020,ari:"Thiswillcauseincreasedrisksinmaternitycomplicationsandpresentchallengestotreatmentandrecovery.",,asignificantincreasedespitethedecliningnumberofmarriedwomenoffertileage,,thesuddenriseinpregnancieshasresultedinmaternityservicescomingundergreaterstrain,andbothfacilitiesandhospitalstaffareunder-resourced,,60percentareage35orolder,whichmeanstheyareconsideredtobeathigherriskduringpregnancy,vedbyAnzhenHospitallastyear,,,manywomenareoptingtohaveanotherchild,accordingtoGu:"Manyofthesepatientsareseekingtreatmentandcareinourhospital,child,andtheirownlivescouldalsobethreatenedduringchildbirth."ConstructionworkersremoveabillboardfromtheroofofabuildingnearTiantanParkinBeijingonNov28.[Photo/Xinhua]TheBeijingcitymanagementauthorityislimitingthenumberandplacementofsignsonbuildingsinorderto"createanurbanskylinethatisvisuallyclearandbright",,,therecanbeonlyonesignwithabuildingsnameonthethirdorhigherstories,ands16districtswilllaunchanenforcementcampaign,thenotificationsaid,andanyfailurebyinstitutionsandindividualstoremove"noncompliant",nearly9,,000signsandbillboardsthatarenon-compliantacrossthecapital,thenewspaperquote,700sig,havingremovedalmost2,willinspectthecapital"roadbyroad",someworriedthatitwillbedifficultforthemtofindtheirdestinations."Sometimes,whenIamlookingforfriendsIhavemadeanappointmentwith,Icaneasilyletthemknowmyexactlocationbytellingthemwhatsignisovermyhead,"saidZhangZhenyu,tlikethefeelingofwalkingnearbuildingswithsignsovertheroofs."Someofthesignsorbillboardshavebeenthereforyearsandtheymayfalldown,"thenetizencommentedonWeibo.

  MadelynRuyle(middle),11,fromtheUnitedStates,isoneof17UnitedNationspandachampions,15ofwhomarevisitingChengdu,Sichuanprovince,,whoaccompaniedher,,fromSudoverf,Russia,wasthrilledtoseelivepandasonMondsappropriatebecauseKalininaisoneof17peoplefrom14,,Nigeria,Britain,Russia,France,Mexico,Columbia,Peru,Jordan,theUnitedStates,SouthKorea,Pakistan,,financedbythebreedingcenter,,listedinternationallyasavulnerablespecies,willhelpthemspreadthewordabouttheUNsustainabledevelopmentgoalsbackathome,,sixstudents,auniversityfacultymember,agovernmentemployee,acommunicationsprofessional,agraphicdesigner,aresearcher,aChinesepaper-cuttingmaster,,twinpandaswhoaretheUNDevelopmentProgramme,the15championswillbeinvolvedintakingcareofpandacubs,engaginginwildernesstrainingtolearnaboutreintroducingcaptivepandastothewildintheDujiangyanFieldCenter,andtrackingwildpandasintheSichuanLongxi-HongkouNationalNatureReserve,accordingtoChenCheng,spokeswomanforthecenter.“Thiswillallowthemtoexperiencethewholeprocessinperson:fromcaptivebreedingtoeffortstoreintroducepandastonature,”thprimaryschoolstudentsinChengdu,,11,,Florida,intheUS,isonherfirstAsiantripandisaccompaniedbyherfather,JimRuyle,thavethem,,andiseagertospreadthewordaboutsustainabledevelopmentgoals,hesaid.ButavisitearlierthisweektoEastChinasAnhuiprovince,whichisamongthetopinlandareasforoutwardmigration,showedthatontheothersideofthecountryseconomicboo,alargemunicipal-levelcitylocatedatmorethan200kilometerstothenorthwestofprovincialcapitalHefei,,,forinstance,moreth,inadjacentDongzhou,ofthesettlements65residents,,chairwomanoftheFuyangWomensFederation,alocalbody,saysthemigrantsmostlymovetowealthierprovincessuchasZhejiangandJiangsu,alsointheeast,andShanghai,workinglow-leveljobsinmanufacturing,services,,179,000childrenundertheageof18havebeenleftbehindhere,hindwiveswhosehusbandshadmigratedfromAnhuiandotherprovincessuchasSichuan,Henan,Guizhou,,en."The2016surveyconsidersthelegalworkingageofyoungChineseandoffamilieswherebothparentshavemigrated,"GuosaysofthedifferencesbetweenthenewcentralgovernmentstudyandACWFlreachesofrelativelyaffluentplacessuchasChongqingandGuangdongprovince.

  LANZHOU,June13(Xinhua)--WiththerapidexpansionofChinaswinemarketinrecentyears,,whohasmanagedwineriesinFrancefor15years,heworldandpeople,withyear-on-yeargrowthofalmost17percent,makingChinathefastestgrowingandfifthlargestmarketworldwide,accordingtoXiKang,co-sponsorandjointvice-chairmanoftheChinaWineAssociationsAlliance."sandalleys,",whicha,professorandassociatedeanoftheCollegeofLifeSciencesofNorthwestNormalUniversity,setupanelectivecoursecalledVintageScienceandWineCulturein2008,sclassinitially,,,therearealsostudentswhowanttogetaqualificationcertificateasawinetasterinthefuture.",Ihopetolearnmoreaboutit,"saidMaYanhong,ngbetween120and1,,anemployeeatwineeducationserviceTastingAnnex,saidthewineindustrywasinarisingperiod,andwinetastingwasingreatneedaswineeducation,production,marketing,hotelsandotherfieldsshowedstrongdemand."Inrecentyears,thosewhocometoapplyforthewine-tasterqualificatiosfordevelopment,"s80sand90sgenerationpursuedahealthyandhigh-qualitylifestyleandhad"astrongerlearningabilityandmoreadvancedconsumptionconcept,"meaningdemandforwinewouldcontinuetogrowinthefuture.FRANKFURT,June13(Xinhua)--GermanautomanufacturerVolkswagenAGannouncedWednesdaytoaccept1billioneuro()fineissuedbylocalpublicprosecutorinthecontextofthedieselgatescandal,rderagainstVolkswagen,whichprovidesforafineof1billioneurointotal,consistingofthemaximumpenaltyaslegallyprovidedforof5millioneurosa,EA288,intheUnitedStatesandinCanada,andEA189,worldwide,wereplacedonthemarketwithanimpermissiblesoftwarefunction,accordingtotheresultsobtainedbytheprosecutor."VolkswagenAGacceptedthefineanditwillnotlodgeanappealagainstit,",Volkswagenadmitteditsresponsibilityforthedieselcrisis,conside,theactiveregulatoryoffeesignificantpositiveeffectsonfurtheractiveadministrativeproceedingsagainstVolkswagendeeplyinvolvedindieselgateinEurope.(1euro=)Enditem

China’sdocumentaryindustryisgrowingsteadilywithdiversebroadcastingplatformsandincreasingappealtotheyoungergeneration,“NewDocumentaryEcologies:Production,DistributionandReception,”gatheredBritishdocumentaryproducerNickFraser,thejurypresidentofthedocumentarycategoryofthefestival’sMagnoliaAwards,ChinesedocumentaryfilmmakerPengHui,andLiBing,,afewacclaimedhomegrowndocumentariesofvariedsubject“TheTaleofChineseMedicine”and"MastersintheForbiddenCity.”Theseproductionshavealsoreceivedhighscoresandarouse“threehighs”(highincome,highculturallevelandhighage)toyoungergroups,anddocumentarieshavechangedfromthe“sidedish”tothe“maindish.”NickFraserbelievesthatChinesedocumentarieshavebrightprospects.“Chinahassomanyimpressivestoriestotell,”Frasersaid.“Thewholesocietyischangingyearbyyear.”Award-winningChinesedocumentar’sfamilyandagroupofvigilanterangersinHohXilinQinghaiProvince.“Inadditiontodocumentingmagnificentsubjectsandevents,documentariesshouldtellreal-lifestoriesofordinarypeople,”,LiBing,directoroftheDocumentaryCenterofYouku,saidtheywillprovidemorerecutting-edgetechnortanceonhowheshootsadocumentary,a:SHINEEditor:ShenKe

  Chinaisacceleratingitsplantocarryoutthe"BroadbandChina"strategytodevelopdigitaleconomy.[Photo/IC]Chinaisacceleratingitsplantocarryoutthe"BroadbandChina"iber,5GnetworksandquantumcommunicationnetworkswerereleasedbytheNationalDevelopmentandReformCommission(NDRC).AccordingtotheNDRC,theopticalfiberprojectwith100MbpcapacitywillbepromotedtoChinavillages,andtheregionssmunicipalities,capitalcitiesandmajorcityclustersinPearlRiver,YangtzeRiverdeltaareas,jing-Tianjin-HebeiregionandtheYangtzeRivereconomiczone,,thebuildingofinformationinfrastructurewillboominruralareasofcentralandwesternregions,andfirst-tiercitieswillenterinto5Gandquantumera,

  BEIJING,June13(Xinhua)--TheStateCouncil,Chinascabinet,onWednesdaydemandedmoreairpo,thecountryshould"furthermarkedlyreducethedensityoffineparticulatematterandthenumberofdaysofheavyairpollutionwithinthreeyears,"saidastatementreleaseda"mainbattlefields"of"thewartodefendtheblueskies"includetheBeijing-Tianjin-Hebeiregionandneighboringareas,andtheYangtzeRiverDeltaregion,,nonewproductioncapacityforsteel,coking,andelectrolyticaluminumwillbeallowed,ragetheeliminationofinlandrivervesselsthathavebeeninuseformorethan20years,,ekeyareasforairpollutioncontrol,andeliminatecoal-burningpower-generationunitsthatdonervision,andgeteveryoneinvolvedtoprotecttheblueskies,thestatementread.FamilybondwithChinapersistsforsixgenerationsRecently,theFleyinWuhan,CentralChina,,,HaworthwasinvitedtothestageatCivicAuditorium,especiallyintheOpticsValleywherehecanseemoreforeignfacesthanever.“"HaworthvisitedWuhanforthefir,Hawort,theHaworthfamilyhasbeenconnectedwithChinaforsixgenerations,thatis,,H,"whenyouweretwo,,youknowthat"ThefirstpagesofhisgrandmothersgrandmothersgrsfatheralsotoldhimthathisgrandmothersnephewusedtohaveextensivebusinesslinkswithChinainthe1990s,whenthereformofmarketeconomyjuststartedinChina."IhavebeentomanyothercitiesinChina,,theinvestmentenvironmentandtherichresourceoftalentsfromuniversities,"saidHaworth.""HaworthalsosaidhehopesthathischildrencancometoChina,learnChinese,andcarryonthefamilytieswithChina."Itwillbetheirhugeadvantageinthefuture."

  坚决反对任何企图在国际上制造“两个中国”“一中一台”和“台湾独立”的行径。

  问题:搜狐是做什么的回答:搜狐公司(NASDAQ:SOHU)是中国社区类/产品领先的互联网品牌,是中国人生活中不可缺少的一部分,搜狐的网络资产以及给众多的SOHU用户在信息、娱乐以及交流方面提供了非常广泛的选择。FRANKFURT,June13(Xinhua)--GermanautomanufacturerVolkswagenAGannouncedWednesdaytoaccept1billioneuro()fineissuedbylocalpublicprosecutorinthecontextofthedieselgatescandal,rderagainstVolkswagen,whichprovidesforafineof1billioneurointotal,consistingofthemaximumpenaltyaslegallyprovidedforof5millioneurosa,EA288,intheUnitedStatesandinCanada,andEA189,worldwide,wereplacedonthemarketwithanimpermissiblesoftwarefunction,accordingtotheresultsobtainedbytheprosecutor."VolkswagenAGacceptedthefineanditwillnotlodgeanappealagainstit,",Volkswagenadmitteditsresponsibilityforthedieselcrisis,conside,theactiveregulatoryoffeesignificantpositiveeffectsonfurtheractiveadministrativeproceedingsagainstVolkswagendeeplyinvolvedindieselgateinEurope.(1euro=)Enditem

  FamilybondwithChinapersistsforsixgenerationsRecently,theFleyinWuhan,CentralChina,,,HaworthwasinvitedtothestageatCivicAuditorium,especiallyintheOpticsValleywherehecanseemoreforeignfacesthanever.“"HaworthvisitedWuhanforthefir,Hawort,theHaworthfamilyhasbeenconnectedwithChinaforsixgenerations,thatis,,H,"whenyouweretwo,,youknowthat"ThefirstpagesofhisgrandmothersgrandmothersgrsfatheralsotoldhimthathisgrandmothersnephewusedtohaveextensivebusinesslinkswithChinainthe1990s,whenthereformofmarketeconomyjuststartedinChina."IhavebeentomanyothercitiesinChina,,theinvestmentenvironmentandtherichresourceoftalentsfromuniversities,"saidHaworth.""HaworthalsosaidhehopesthathischildrencancometoChina,learnChinese,andcarryonthefamilytieswithChina."Itwillbetheirhugeadvantageinthefuture."

  令人惊喜的是,跑完五公里的王鸥看上去状态非常不错,她坦言:“其实还蛮过瘾的,因为最初以为连一公里都坚持不下来,没想到最后成功超越了自己。

  ConstructionworkersremoveabillboardfromtheroofofabuildingnearTiantanParkinBeijingonNov28.[Photo/Xinhua]TheBeijingcitymanagementauthorityislimitingthenumberandplacementofsignsonbuildingsinorderto"createanurbanskylinethatisvisuallyclearandbright",,,therecanbeonlyonesignwithabuildingsnameonthethirdorhigherstories,ands16districtswilllaunchanenforcementcampaign,thenotificationsaid,andanyfailurebyinstitutionsandindividualstoremove"noncompliant",nearly9,,000signsandbillboardsthatarenon-compliantacrossthecapital,thenewspaperquote,700sig,havingremovedalmost2,willinspectthecapital"roadbyroad",someworriedthatitwillbedifficultforthemtofindtheirdestinations."Sometimes,whenIamlookingforfriendsIhavemadeanappointmentwith,Icaneasilyletthemknowmyexactlocationbytellingthemwhatsignisovermyhead,"saidZhangZhenyu,tlikethefeelingofwalkingnearbuildingswithsignsovertheroofs."Someofthesignsorbillboardshavebeenthereforyearsandtheymayfalldown,"thenetizencommentedonWeibo.BernardCharles,chiefexecutiveofficerofsoftwarecompanyDassaultSystemes.[Photo/VCG]Thebeautyofvirtualrealityisthatithelpsyouimagineabetterworldevenifyoudontknowhowtoachieveit,saystheheadofFrenchsoftwarefirmDassaultSystemesWhenBernardCharleslandsinBeijing,,hisChinese"contact",WeChata,includingaviation,andwasinvolvedinChinasfirsthomegrownlargepassengerjet,theC919,whichmadeitsmaidenflightinMay."Whenwesetupacollaborativeplatformtohelpdevelopthenext-generationcivilaircraftinthecountry,weworkedwithsuppliersfromEuropeancountriesandothernations,"Charlessaid."BymakingthemvisibletonewclientsinChina,wearebuildingavirtualbelttoconnectthemhere,",DassaultSystemesisbasedinVelizy-VillacoublayinthesouthwesternsuburbsofParisandhasamarketcapitalizationof$,,000andaclientlistwhichincludesChinasleadingaircraftmanufacturer,CommercialandAircraftCorpofChinaLtd,,theworld,thesoftwaregiantislookingtoincreaseitspresencehere."Wewanttobethecatalystandenablerof(helpingtotransform)manufacturing,",hewentontotalkaboutDassaultSystemesadeaspeechattheBoaoForumin2015,forusthatthedoor,globalizationbringschallengestotheworldbutitalsohelpsi,thewinnersarenotthosewithbigslicesofthemarket,ativ,itisquitedifficultforalotofFrenchsmall-andmedium-sizedenter,sfutureprospectsinChinaTheneedforthecountrytotransformthemanufacturing,wewanttobethebest"catalystandenabler"of(helpingto),,andmanufacturingprogramsinEuropeandtheUnitedStatesTheyal-,b,intermsofmanufacturing,atithelpsyouimagineabetterworldevenifyoudones,suchasenvironmentaldegradation,,onbases,,theworldistransportingmanythings,suchasrawmaterialsandwaste,everyday,,,wecanliftthemfivetimeslessinrealitybyusingVR(toscaneveryangleoftheproducts).ThatsavestimeandenergyespeciallyinChina,stechnologyisusedindifferentindustries,,itisnotonlyaboutwhatwecando,,butifweunderstandwhatisvaluable,andifwebelievewecandoitbetter,thenwehavetotry(tobethebest).Sinceyoutookover,DassaultSystemeshasgoneonabuyingspree,buthowdoyouintegratethosecompaniesintothegroupWearealwaysatadisadvantagecomparedtoourcompetitors,especiallythosefromtheUS,,welearnhowtodobusinessindifferentcountries,,ifyouwanttoconvincesomeonetobewithyou,-,,,ourcustomersareverystrong,yimportanttoacompany(tendto),,,suchasvisitingmuseums,:60Nationality:FrenchCareer:2016:vice-chairmanandCEOofDassaultSystemes1995:presidentandCEOofDassaultSystemes1988:promotedtopresidentofstrategy,researchanddevelopmentatDassaultSystemes1983::AgraduateoftheEcoleNormaleSuperieureengineeringschoolinCachanandaPhDinmechanicalengineering,:Marriedwithfivechildren

  

  金曼:歌剧是一种共情 当下作品应是未来传统

 
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血友病人似“玻璃人” 大多数是家族遗传

时间:2019-09-22 00:13  来源:新快报
FamilybondwithChinapersistsforsixgenerationsRecently,theFleyinWuhan,CentralChina,,,HaworthwasinvitedtothestageatCivicAuditorium,especiallyintheOpticsValleywherehecanseemoreforeignfacesthanever.“"HaworthvisitedWuhanforthefir,Hawort,theHaworthfamilyhasbeenconnectedwithChinaforsixgenerations,thatis,,H,"whenyouweretwo,,youknowthat"ThefirstpagesofhisgrandmothersgrandmothersgrsfatheralsotoldhimthathisgrandmothersnephewusedtohaveextensivebusinesslinkswithChinainthe1990s,whenthereformofmarketeconomyjuststartedinChina."IhavebeentomanyothercitiesinChina,,theinvestmentenvironmentandtherichresourceoftalentsfromuniversities,"saidHaworth.""HaworthalsosaidhehopesthathischildrencancometoChina,learnChinese,andcarryonthefamilytieswithChina."Itwillbetheirhugeadvantageinthefuture."

新快报讯 记者梁瑜报道 为了血友病的儿子不容易受伤,再热的天,他们都要儿子带着头盔,因为一旦撞击受伤就会出血不止,无穷尽的烦恼就会衍生。4月17日是“世界血友病日”,广州市慈善会与南方医科大学南方医院、拜耳公司共同在广州南方医院广场举办血友病患者联谊活动,血液科专家指出,血友病是一种罕见的遗传性凝血障碍疾病,患者被称为“玻璃人”,家族中有疾病史的,女孩应注意筛查,避免影响下一代。

治疗护理恰当

血友病患者可健康生活

南方医科大学南方医院血液科孙竞教授指出,血友病主要影响男性,患者血液中缺少功能正常的凝血因子Ⅷ(甲型血友病或典型血友病)或因子Ⅸ(乙型血友病或克雷司马斯病),85%的患者血属于前者。血友病可引起出血时间延长或者自发性出血,尤其是肌肉、关节和内部器官出血。通过治疗和适当的护理,血友病患者可以健康地生活;不进行治疗的话,血友病会导致剧痛、严重关节损伤、残疾、甚至死亡。其严重程度由患者体内的凝血因子水平决定。

目前,我国针对血友病患者主要使用低剂量预防或按需治疗方案(即发现出血后再注射凝血因子),患者长期使用后能减少出血的发生,但关节严重损害的比例却高达75%-90%。“由此可见,这种治疗方法是不够的。”孙竞认为,应按照足剂量的预防治疗方案给患者注射补充正常人所需量的人凝血因子Ⅷ产品,可以把出血次数控制在每年5次以下,即使是重度甲型血友病患者,也可以过上几乎和正常人一样的生活。

家族中有血友病的女性

建议做筛查

血友病具有遗传性,大多数患者生来患病且有家族史,女性通常作为血友病基因携带者将基因遗传给下一代,男性则会发病,即人们所说的“传男不传女”。大约每5000-10000个男性中就有一个血友病甲患者。

血友病具有X染色体相关的隐性特征,从双亲之一传给孩子:当父亲患有血友病而母亲未患此疾病时,男孩子不会出现血友病,所有的女孩将携带血友病基因,尽管其不受疾病的影响;血友病携带者女性将基因传给孩子,当母亲是携带者而父亲不是血友病患者时,每个男孩都有50%的几率患血友病,而每个女孩都有50%的几率成为携带者。然而,也有可能基因出现自发突变,在约30%的病例中无确切的家族遗传史。

因此,他建议,只要家族中有血友病的,所有女性都建议筛查,“筛查只要验血即可。”据了解,“为生命续航——血友病患者援助项目”自2011年启动,2015年项目救助范围由儿童扩大至成年人,2016年开始推行“一站式结算”,由南方医院按照救助标准先行垫付医疗费用,再由市慈善会将患者援助款定期划拨至医院,实现受助患者“随来随看,随走随结”。

编 辑:刘明远
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